Isolated Double-Chambered Right Ventricle: A Rare Congenital Heart Disease

Sofia Bezza *

Department of Cardiology, Mohammed VI University Hospital, Marrakesh, Morocco.

Mohamed Imad Rhoujjati

Department of Cardiology, Mohammed VI University Hospital, Marrakesh, Morocco.

Mohammed Eljamili

Department of Cardiology, Mohammed VI University Hospital, Marrakesh, Morocco.

Saloua El Karimi

Department of Cardiology, Mohammed VI University Hospital, Marrakesh, Morocco.

Mustapha Elhattaoui

Department of Cardiology, Mohammed VI University Hospital, Marrakesh, Morocco.

*Author to whom correspondence should be addressed.


Abstract

Double-chambered right ventricle (DCRV) is an uncommon congenital heart condition characterized by a progressive obstruction in the right ventricular outflow tract. This obstruction is caused by anomalous muscles or fibrous tissues that divide the right ventricle into two cavities: a proximal high-pressure chamber (anatomically lower) and a distal low-pressure chamber (anatomically higher). We present a case of a middle-aged man with a medical history of recurrent symptomatic dyspnea. Upon presentation, there were no signs of congestive cardiac failure. The diagnosis was confirmed using transthoracic two-dimensional (2-D) echocardiography and Transesophageal echocardiography (TEE) for more precise characterization. The primary objective of this case report is to highlight the rarity of this congenital heart disease, particularly in adults.

Keywords: Double-chambered right ventricle, adult congenital heart disease, right ventricular outflow tract obstruction, echocardiography


How to Cite

Bezza, S., Rhoujjati, M. I., Eljamili , M., Karimi, S. E., & Elhattaoui, M. (2024). Isolated Double-Chambered Right Ventricle: A Rare Congenital Heart Disease. Cardiology and Angiology: An International Journal, 13(1), 1–4. https://doi.org/10.9734/ca/2024/v13i1385

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