A Rare Case of Pulmonary Arterial Hypertension as the Initial Presentation of Systemic Lupus Erythematosus in a Pediatric Patient
Prasad Jain
*
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Kalyan Munde
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Anant Munde
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Hariom Kolapkar
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Khalel Ahmed
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Anil Kumar Gupta
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
Vighnesh Rane
Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.
*Author to whom correspondence should be addressed.
Abstract
Pulmonary hypertension (PH) diagnosis can be challenging, particularly in young patients with systemic lupus erythematosus (SLE). We report a 10-year-old female presenting with suspected sinus venosus atrial septal defect (ASD) with Eisenmengerisation, later diagnosed with primary pulmonary arterial hypertension (PAH) secondary to SLE. She received vasodilators and immunosuppressants, showing partial treatment response.
Keywords: Sinus venosus, pulmonary hypertension, antibodies, atrial septal defect, SLE