A Rare Case of Pulmonary Arterial Hypertension as the Initial Presentation of Systemic Lupus Erythematosus in a Pediatric Patient

Prasad Jain *

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Kalyan Munde

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Anant Munde

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Hariom Kolapkar

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Khalel Ahmed

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Anil Kumar Gupta

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

Vighnesh Rane

Department of Cardiology, GGMC & JJ Hospital, Mumbai, India.

*Author to whom correspondence should be addressed.


Abstract

Pulmonary hypertension (PH) diagnosis can be challenging, particularly in young patients with systemic lupus erythematosus (SLE). We report a 10-year-old female presenting with suspected sinus venosus atrial septal defect (ASD) with Eisenmengerisation, later diagnosed with primary pulmonary arterial hypertension (PAH) secondary to SLE. She received vasodilators and immunosuppressants, showing partial treatment response.

Keywords: Sinus venosus, pulmonary hypertension, antibodies, atrial septal defect, SLE


How to Cite

Jain, Prasad, Kalyan Munde, Anant Munde, Hariom Kolapkar, Khalel Ahmed, Anil Kumar Gupta, and Vighnesh Rane. 2024. “A Rare Case of Pulmonary Arterial Hypertension As the Initial Presentation of Systemic Lupus Erythematosus in a Pediatric Patient”. Cardiology and Angiology: An International Journal 13 (4):50-53. https://doi.org/10.9734/ca/2024/v13i4439.