A Young Healthy Woman with Supraventricular Tachycardia Reveals an Underlying Left Ventricular Non-compaction Cardiomyopathy: A Rare Case Report

A. Fadoul Tahir

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco.

M. Njie *

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco.

P. M. Mulendele

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco.

M. Foudail

Department of Polyvalent Medicine, Subsection Cardiology, Hospital Centre of Vire, Normandie, France.

M. Haboub

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco and Professor at the Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco.

S. Arous

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco and Professor at the Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco.

M. Ghali Benouna

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco.

A. Drighil

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco and Professor at the Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco.

L. Azzouzi

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco and Professor at the Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco.

R. Habbal

Department of Cardiology P37, Ibn Rochd University Hospital, Casablanca, Morocco and Professor at the Faculty of Medicine and Pharmacy, Hassan II University of Casablanca, Casablanca, Morocco.

*Author to whom correspondence should be addressed.


Abstract

LVNC (left ventricular non-compaction) is a rare congenital cardiomyopathy with a reported incidence of 0.05% in adults. It can occur in isolation or affect both ventricles. It’s characterized by prominent LV trabeculae and deep intertrabecular recesses which are filled with blood from the ventricular cavity without evidence of communication to the epicardial coronary artery system. Frequent premature supra ventricular tachycardia as unique finding in LVNC cardiomyopathy is rare manifestation of this disease. We report a case of a frequent persistent supraventricular tachycardia as first manifestation of a patient with LVNC cardiomyopathy in a young healthy woman who despite radio frequency ablation therapy of the supraventricular tachycardia remains symptomatic. The patient was later placed on medical therapy based on a non-cardio selective beta-blocker with a good clinical outcome without recurrent of supra-ventricular arrythmias.

Keywords: Left ventricular non-compaction, supra-ventricular tachycardia, premature ventricular complexes, beta-blockers


How to Cite

Tahir, A. F., Njie , M., Mulendele , P. M., Foudail , M., Haboub , M., Arous , S., Benouna , M. G., Drighil , A., Azzouzi , L., & Habbal , R. (2023). A Young Healthy Woman with Supraventricular Tachycardia Reveals an Underlying Left Ventricular Non-compaction Cardiomyopathy: A Rare Case Report. Cardiology and Angiology: An International Journal, 12(3), 19–25. https://doi.org/10.9734/ca/2023/v12i3319

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