Dilated Cardiomyopathy with Biventricular Thrombi: A Severe Manifestation of Behcet Disease
Junior Rocyr Ibara-Onguema *
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
Franck Bienvenu Ekoba Othende
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
Tibou Camara
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
Mohammed El Jamili
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
Saloua El Karimi
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
Mustapha El Hattaoui
Department of Cardiology and Vascular Disease, Mohammed VI Hospital and University Center of Marrakech, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Behcet’s disease is a systemic vasculitis of the vessels for all calibers, touching arterial and venous territories. The causes of disease are unknow. BD reaches young age subjects from 10 to 45 years and affects both men and women. BD is ubiquitous but more frequent in patients from Mediterranean basin, the middle East and Asia. The diagnosis of BD is essentially clinical. The diagnostic criteria make it possible to carry the diagnosis with good sensitivity and specifity. BD evolves by recurrent inflammatory attack. BD can affect all of the organs; cardiacs manifestations are dominated by intracardiac thrombosis, the damage of three tunics, coronaryarteritis with or without myocardial infarction, coronaries aneurysms and endomyocardial fibrosis. The vascular manifestations are dominated by arterial or venous thrombosis. The presence of dilated cardiomyopathy with reduced left ventricular ejection fraction is rare. It can be explained by ischemic or inflammatory origin by cytokines. We report a case of young woman aged of 33 years to the history of 3 episodes of bipolar aphtae which presented dilated cardiomyopathy with reduced left ventricular function, biventricular thrombosis, bilateral distal pulmonary embolism with pulmonary infarction.
Keywords: Dilated cardiomyopathy, Behcet disease, thrombus, left ventricular dysfonction