Left Ventricular Non-Compaction Cardiomyopathy: Case Report and Review of Literature

B. Maatof

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

I. Hazzazi *

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

H. Nabawi

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

M. Eljamili

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

S. El Karimi

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

M. Elhattaoui

Department of Cardiology, Mohammed VI University Hospital Center, Marrakesh, Morocco.

*Author to whom correspondence should be addressed.


Abstract

Non-compaction cardiomyopathy (NCC) is characterized by trabeculations in either one or both ventricles. Clinical presentation is highly variable: dyspnea, palpitation, thromboembolic events, arrhythmia, or sudden cardiac death. There are currently no universally-accepted criteria for classifying and diagnosing left ventricular non-compaction (LVNC) cardiomyopathy. Transthoracic echocardiography (TTE) is the diagnostic exam of choice. The diagnosis is often missed or delayed because of a lack of knowledge about this uncommon disease. Progression of LVNC is highly variable and prognosis is very difficult to predict.

We report a case of a 50-year-old female patient with a history of total thyroidectomy under hormonal supplementation who consults for dyspnea and paroxysmal palpitations revealing an isolated LVNC.

This case emphasizes the importance of imaging techniques, which are, TTE and cardiac magnetic resonance imaging (MRI) in early diagnosis, management, and follow-up.

Keywords: Cardiomyopathy, left ventricular non-compaction cardiomyopathy, cardiac magnetic resonance imaging, ventricular trabeculations, spongy myocardium


How to Cite

Maatof, B., I. Hazzazi, H. Nabawi, M. Eljamili, S. El Karimi, and M. Elhattaoui. 2023. “Left Ventricular Non-Compaction Cardiomyopathy: Case Report and Review of Literature”. Cardiology and Angiology: An International Journal 12 (3):121-28. https://doi.org/10.9734/ca/2023/v12i3334.

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