Acquired Extrinsic Pulmonary Stenosis Secondary to a Compressing Mediastinal Tumor
M. Naaim *
Cardiology Department, ARRAZI Hospital, Mohammed VI University Hospital, Marrakech, Morocco.
F. Rebbouh
Cardiology Department, ARRAZI Hospital, Mohammed VI University Hospital, Marrakech, Morocco.
M. Eljamili
Cardiology Department, ARRAZI Hospital, Mohammed VI University Hospital, Marrakech, Morocco.
S. El Karimi
Cardiology Department, ARRAZI Hospital, Mohammed VI University Hospital, Marrakech, Morocco.
M. El Hattaoui
Cardiology Department, ARRAZI Hospital, Mohammed VI University Hospital, Marrakech, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Acquired pulmonary stenosis in adults due to extrinsic compression of the pulmonary artery is a rare manifestation of non-Hodgkin’s lymphoma (NHL). The incidence remains poorly known in the literature since only a few sporadic cases are described.
The clinical management is directed towards the treatment of the underlying disease. According to the latter, the patient may benefit from chemotherapy, radiotherapy, angioplasty, stenting, or surgery.
We describe here the case of a young patient who was diagnosed with acquired extrinsic pulmonary stenosis secondary to a type B large cell lymphoma of mediastinal location. Our clinical case affirms the interest of a transthoracic echocardiogram in the diagnosis as well as the follow-up of this unusual manifestation.
Keywords: Pulmonary stenosis, mediastinal tumor, lymphoma, transthoracic echocardiogram
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References
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